This report presents a patient with longstanding dysphagia and anaemia in whom a posterior pharyngeal web was shown. The investigations were widened, therefore, in the hope that we could find an explanation for the link between sideropenic dysphagia. Dysphagia either refers to the difficulty someone may have with initiating a swallow. Esophageal webs are an infrequent cause of dysphagia. Fulfilling the classical triad of dysphagia, irondeficiency anaemia and upper oesophageal webs, plummervinson syndrome or patersonbrown kelly syndrome, sideropenic dysphagia was diagnosed. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 toll free. A 43yearold woman with a history of recurrent median cervical cyst, treated operatively 2 years earlier by thyroglossal duct excision. Links to pubmed are also available for selected references. In case of significant obstruction of the esophageal lumen by esophageal web and persistent dysphagia. Additional features are glossitis, angular cheilitis and koilonychia. Plummervinson syndrome is a condition that can occur in people with longterm chronic iron deficiency anemia. In subsequent endoscopy, the webs were dilated with considerable resultant improvement in her dysphagia. Oxford, england the syndrome of dysphagia, glossitis, koilo nychia and iron deficiency anaemia is known by several names including the paterson kelly syndrome 1,2, the plummervinson syndrome 3 and sideropenic dysphagia 4. Dec 01, 2009 sideropenic dysphagia sideropenic dysphagia zimmer, vincent.
Plummer disease hyperthyroidism resulting from a nodular toxic goiter, usually not accompanied by exophthalmos. Plummervinson syndrome iron deficiency anemia, dysphagia, esophageal web, and atrophic glossitis. Chronic iron deficiency anemia may manifest as plummervinson syndrome pvs, also called patersonbrownkelly syndrome or sideropenic dysphagia, which is the classical triad of dysphagia. The term sideropenic dysphagia has also been used, since the syndrome can occur with iron deficiency sideropenia, but it is not as. Siderophile element article about siderophile element by. Register for a free account existing user log in existing user log in. This site is like a library, use search box in the widget to get ebook that you want. Plummervinson syndrome pvs also known as patersonkelly syndrome or sideropenic dysphagia 1 is characterized by dysphagia, iron deficiency anemia and upper esophageal webs. Most of the patients are white middleaged women, in the fourth to seventh decade of life, but the isderopenica has also been described in children and adolescents.
A 43yearold woman with a history of recurrent median cervical cyst, treated operatively 2 years earlier by thyroglossal duct excision with partial hyoid resection, presented to our otolaryngology clinic due to. Plummer 18741937 and surgeon porter p vinson 18901959. Serial contrasted gastrointestinal radiography or uppergastrointestinal endoscopy. As the condition progresses, more severe symptoms may be experienced, such as shortness of breath, pounding of the heart, and a rapid pulse. Aug 07, 2019 kellypaterson syndrome sideropenic dysphagia prevalence. Also known as sideropenic dysphagia and, in the uk, as patersonkelly syndrome.
Anemia in this patient population requires careful evaluation of multiple organ systems. Click download or read online button to get the source for pediatric dysphagia book now. Anemia is defined as a decrease in the number of red blood cells or the amount of hemoglobin in the blood. Sep 01, 2006 if you have problems viewing pdf files, download the latest version of adobe reader. When onset is slow, symptoms are often vague such as feeling tired, weak, short of breath, or having decreased ability to exercise. The source for pediatric dysphagia download ebook pdf. The investigations were widened, therefore, in the hope that we could find an explanation for the link between sideropenic dysphagia and hiatus hernia.
The source for pediatric dysphagia download ebook pdf, epub. Even though the syndrome is very rare nowadays, its recognition is important because it identifies a group of patients at increased risk of squamous cell carcinoma of the pharynx and the esophagus. Plummervinson syndrome iron deficiency anemia, dysphagia. This diet consists of pureed, homogenous, and cohesive foods. The association of postcricoid dysphagia, upper esophageal webs, and iron deficiency anemia is known as plummervinson syndrome pvs in the united states and patersonbrown kelly syndrome in the united kingdom. Plummervinson syndrome pvs, also called patersonbrownkelly syndrome or sideropenic dysphagia, is a rare disease characterized by. This syndrome is also known as sideropenic dysphagia which implies the burning sensation or throat pain while swallowing. Pdf oral submucous fibrosisa case report semantic scholar. In two cases, an associated squamous cell cancer was diagnosed 20, 29. Guidance for medication assessment in patients with swallowing dysphagia or feeding disorders pharmacy benefits managementstrategic healthcare group pbm june 2006 the purpose of this clinical guidance is to provide pharmacists in the va with the information needed to conduct a medication regimen assessment for a patient with. Some people may be completely unable to swallow or may have trouble safely swallowing liquids, foods, or saliva. Dysphagia screening in stroke patients is critical in order to prevent adverse outcomes related to aspiration and inadequate hydrationnutrition 5.
Sideropenic dysphagia in a patient with ulcerative colitis. We have studied oropharyngeal and esophageal transits and esophageal contractions of adult patients with iron deficiency. The practice portal, asha policy documents, and guidelines contain information for use in all settings. The patients were free of relevant dysphagia during the followup period. Sideropenic dysphagia sideropenic dysphagia zimmer, vincent. Up to 50% of parkinson patients show some symptoms consistent with oropharyngeal dysphagia, and up to 95% are found to have abnormalities on video. Plummervinson syndrome is defined by the classic triad of dysphagia, irondeficiency anemia and esophageal webs. Irondeficiency anemia is anemia caused by a lack of iron. Plummer dilator an instrument for dilating the lower end of the esophagus in cardiospasm. Sideropenic dysphagia definition of sideropenic dysphagia. Vena diploica frontal a etiology the etiopathogenesis of plummervinson syndrome is unknown. Our preliminary work revealed the coexistence of the two disorders in a number of patients. Sideropenic dysphagia see related article, lenz p et al, on page e72 in cgh.
We read with interest the paper by rodriguez et al. Other patients studied after that also had low contraction amplitude. The nature and treatment of pulmmervinson dysphagia. Sideropenic dysphagia and hiatus hernia sciencedirect.
Plummervinson syndrome with concomitant factor vii. Three to 15 per cent of the patients with plummervinson. Most of the patients are white middleaged women, in. Since the dysphagia is associated with iron deficiency anaemia, the term sideropenic dysphagia has often been used to describe this condition. Scribd is the worlds largest social reading and publishing site. Treatment with iron supplementation and mechanical widening of the esophagus generally provides an excellent outcome. Blood tests demonstrate a hypochromic microcytic anemia that is consistent with an irondeficiency anemia. Dysphagia, iron deficiency anemia, plummervinson syndrome. If you have access to a journal via a society or association membership, please browse to your society journal, select an article to view, and follow the instructions in this box. Sideropenic anemia article about sideropenic anemia by. Videofluoroscopy revealed a postcricoid web arising from the anterior wall and passing over into a. Treatment is iron supplementation and, if need be, dilation of the web to permit normal swallowing and the passage of food. Click on any term below to browse the alphabetical index. Plummervinson syndrome is a condition that affects mostly middle aged caucasian women and is defined by the triad of iron deficiency anemia, upper esophageal webs and postcricoid dysphagia.
Esophageal rings and webs sideropenic dysphagia or plummervinson. Sideropenic dysphagia definition by babylons free dictionary. People with this condition have problems swallowing due to small, thin growths of tissue that. Sideropenic dysphagia, previously referred to as the plummer. Plummer vinson syndrome, also known as patterson kelly brown syndrome, sideropenic dysphagia, hysterical dysphagia is a premalignant condition, in which the patient has iron deficiency anemia. A 43yearold woman with a history of recurrent median cervical cyst, treated operatively 2 years earlier by thyroglossal duct excision with partial hyoid resection, presented to our otolaryngology clinic due to progressive cervical dysphagia for solid foods and a weight loss of 10 kg. Summary epidemiology sideropeenica data about the epidemiology of the syndrome are not available. Very often the nails are not concave but show a definite tendency to split up and break at the free edge. Pdf fact sheet on sideropenic dysphagia researchgate. Plummervinson syndrome has been identified as a risk factor for developing squamous cell carcinoma of the upper gastrointestinal tract. The term sideropenic dysphagia has also been used, since the syndrome can occur with iron deficiency sideropenia, but it is not associated with anemia. Serial contrasted gastrointestinal radiography or uppergastrointestinal endoscopy may reveal the web in the esophagus. If you have access to a journal via a society or association membership, please browse to your society journal, select an article to. Symptoms resulting from anemia weakness, pallor, fatigue, tachycardia may dominate the clinical picture.
People with dysphagia have dificulty swallowing and may even experience pain while swallowing odynophagia. For deficiency states, replacement therapy is used to combat the specific deficiency, e. The term sideropenic dysphagia is sometimes used for the disorder simply because irondeficiency or sideropenia is a key factor in the. Aug 17, 2019 additional features are glossitis, angular cheilitis and koilonychia.
The first retrospective study included 507 children aged 1 to 24 months with sideropenic anemia who were hospitalized at the institute of child and youth healthcare of vojvodina, department for infant. Dysphagia and oesophageal web in sideropenic anaemia. Oxford, england the syndrome of dysphagia, glossitis, koilo nychia and iron deficiency anaemia is known by several names including the paterson kelly syndrome 1,2, the plummervinson syndrome 3 and sideropenic dysphagia. The plummervinson syndrome is characterized by dysphagia, irondeficiency anemia, and esophageal webs. Sideropenic dysphagia tabular list of diseases and injuries the tabular list of diseases and injuries is a list of icd10 codes, organized head to toe into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The roentgenological diagnosis of sideropenic dysphagia. Even small amounts of gluten cause relapse in children with celiac disease. In case of significant obstruction of the esophageal lumen by esophageal web and persistent dysphagia despite iron supplementation, rupture and dilation of the web are necessary. And in one case a gastric cancer was found by endoscopy one year after the diagnosis of plummervinson syndrome. The improvement in dysphagia after iron therapy provides evidence for an association between iron deficiency and postcricoid dysphagia. The topic sideropenic dysphagia you are seeking is a synonym, or alternative name, or is closely related to the medical condition plummervinson syndrome. A case of sideropenic dysphagia is described in a patient with ulcerative colitis.
Dysphagia is usually classified as orophayngeal dysphagia which produced by an abnormality in the preparation or transfer of food from mouth to upper esophagus, this may occur as a result of poor motor control of the toung, jaw or other oral structures or maybe due to abnormalities in swallowing reflex. Technical report pdf available march 2015 with 672 reads. Feb 14, 2019 the association of postcricoid dysphagia, upper esophageal webs, and iron deficiency anemia is known as plummervinson syndrome pvs in the united states and patersonbrown kelly syndrome in the united kingdom. Pdf file of the complete article 968k, or click on a page image below to browse page by page. The term sideropenic dysphagia has also been used, since the syndrome can occur with iron deficiency sideropenia. Registered users can save articles, searches, and manage email alerts. The dysphagia is usually painless and intermittent or progressive over years, limited to solids and sometimes associated with weight loss. Not only does eating provide nutrients, but it also serves as important role in social interaction. Introduction sideropenic dysphagia, also called plummervinson syndrome pvs or patersonbrownkelly syndrome, is a rare disease characterised by dysphagia difficulty in. Up to 50% of parkinson patients show some symptoms consistent with oropharyngeal dysphagia. Apr 03, 2019 disfagia sideropenica pdf anemia sideropenica hover over links in text for more info. Pdf endoscopic management of dysphagia in plummervinson. Even though the syndrome is very rare nowadays, its recognition is.
Access to society journal content varies across our titles. Sideropenic dysphagia in an adolescent request pdf. Sideropenic anemia definition of sideropenic anemia by. Introduction hand, it refers to a patients awareness of impaire swallowing is a complex function that affects the physical and mental health of all human beings. In 1993 we published a case report of a woman with iron deficiency and dysphagia who had low contraction amplitude in the esophageal body. Sideropenic definition of sideropenic by the free dictionary. Sideropenic dysphagia in a patient with ulcerative colitis ralph wright, m. With iron replacement the amplitude increased and the patient was free from dysphagia. Figure 3 from oral submucous fibrosisa case report. Plummer vinson syndrome also known as paterson brownkelly syndrome is a syndrome associated with the triad of symptoms comprising microcytic hypochromic anemia, oesophageal strictures, and dysphagia. Difficulty in swallowing or dysphagia is a common symptom. Kellypaterson syndrome sideropenic dysphagia prevalence.
Plummervinson syndrome pvs, also called patersonbrownkelly syndrome or sideropenic dysphagia is an extremely rare syndrome which includes. Vinson syndrome pvs is characterized by dysphagia due to upper esophageal or hypopharangeal web in patients with chronic iron. Sideropenia definition of sideropenia by the free dictionary. Plummer vinson syndrome in a 6 year old boy medcrave online. Guidance for medication assessment in patients with. Pdf plummervinson or patersonkelly syndrome presents as a classical triad. Pdf introduction sideropenic dysphagia, also called plummervinson. Sideropenic dysphagia article about sideropenic dysphagia. For language access assistance, contact the ncats public information officer. People with this condition have problems swallowing due to small, thin growths of tissue that partially block the upper food pipe esophagus. The term sideropenic dysphagia has also been used, because the syndrome can occur with iron deficiency sideropenia, but it is not associated with anemia. Given that it can involve iron deficiency sideropenia without anemia, it has been also called sideropenic dysphagia.
The most usual presenting symptom the dysphagia can be intermittent or progressive through the years. Mild degrees of anemia often cause only slight and vague symptoms, perhaps nothing more than easy fatigue or a lack of energy. Dec 21, 2018 read medical definition of sideropenic dysphagia. And in one case a gastric cancer was found by endoscopy one year after the diagnosis of plummervinson syndrome 34. Pdf file of the complete article 768k, or click on a page image below to browse page by page. Plummervinson syndrome is a rare disease characterized by difficulty swallowing, irondeficiency anemia, glossitis, cheilosis and esophageal webs. Biopsy of involved mucosa typically reveals epithelial atrophy shrinking and varying amounts of submucosal chronic inflammation. Click download or read online button to get the source for pediatric dysphagia.
782 1382 124 358 1542 1261 116 762 1205 352 1295 1377 967 644 702 534 1254 1346 992 345 694 861 90 1264 206 598 646 1335 1495 528 1334 732 871 1108 915 1040 136 251 758 939 609